Total Pulmonary Artery Atresia Associated with Abnormal Pulmonary Venous Drainage as a Rare Presentation of Scimitar Syndrome

Total Pulmonary Artery Atresia Associated with Abnormal Pulmonary Venous Drainage as a Rare Presentation of Scimitar Syndrome

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Scimitar syndrome or pulmonary venolobar syndrome is a rare, complex, and LCD/LED Display Panels variable malformation of the right lung characterized by an abnormal right sided pulmonary drainage into the inferior vena cava, malformation of the right lung, abnormal arterial supply, and sometimes cardiac malformation.Despite the varying degrees of pulmonary hypoplasia and pulmonary artery hypertension, about half of the patients with scimitar syndrome are asymptomatic or mildly symptomatic when the diagnosis is made.Neonates have severe symptoms and worse prognosis while older children come to light because of recurrent respiratory infections, heart murmur, FUNCTION TEA or an abnormal chest radiograph.